Abstract

A CASE REPORT ON KAWASAKI DISEASE (MUCOCUTANEOUS LYMPH NODE SYNDROME)

Diya Shibuchan*, Neha Maria Augustine, Femy Thomas, Arya Ponnappan and Christeena Mariyam Baby

Abstract

Background: Kawasaki disease (KD),also known as mucocutaneous lymph node syndrome, is an acute febrile illness of early childhood which is characterized by vasculitis of the medium-sized arteries. KD is a rare condition with acute, systemic inflammatory process that causes fever, exanthematous rashes and vascular disease. The rare nature and unknown etiology is one of the pitfalls that leads to misdiagnosis and has complication like coronary artery aneurysm. The diagnosis of KD still depends on the clinical criteria that include fever for 5 days or longer and at least 4 of the following: Bilateral non purulent conjunctivitis, peripheral extremities changes including edema or desquamation, polymorphous rash, oral mucous membrane changes such as fissured lips, or strawberry tongue, and acute cervical lymphadenopathy. Case report: This is a case report of a KD where, a seven year old boy, presented with prolonged fever, rashes all over the body, cervical lymph node enlargement, dry fissured lips, periungual peeling, bilateral non purulent conjunctivitis, strawberry tongue. He was fully investigated and was treated with intravenous immunoglobulin and aspirin. Conclusion: Any child with suspected KD should have to receive prompt diagnosis and early initiation of intravenous immunoglobulin and aspirin therapy are of utmost importance in preventing coronary complications.

Keywords: Kawasaki disease, Vasculitis, Coronary aneurysms, Intravenous immunoglobulin.