Abstract

COMPLETE ATRIOVENTRICULAR BLOCK IN CARDIAC AMYLOIDOSIS: UNUSUAL PATTERN OF REVELATION

M. Boumaaz*, S. Ahchouch, M. Malki, A. Zaimi, I. Asfalou and A. Benyass

.

Abstract

Cardiac involvement is frequent in systemic amyloidosis and is a major determinant of treatment options and prognosis. It may occur in the three main types of amyloidosis, and include diastolic followed by systolic heart failure, atrial and/or ventricular arrhythmias, embolic events and sometimes conduction disturbances with sudden death. Complete atrioventricular block is an unusual pattern of revelation of this disease as described on this case report. This disturbance can be due to infiltrative destruction of the conduction system by amyloid; but also; it can result from diffuse or focal occlusion of the vessels supplying the specialized conduction system. The purpose of this work is to alarm the clinician about the significant risk of conduction disturbances in a patient with amyloidosis; as well as to highlight the interest of seeking, preventing and treating these disorders, and this by electrocardiogram, holters, or even endocavitary explorations.

Keywords: Complete atrioventricular block; Cardiac amyloidosis; echocardiogram, pattern.