Abstract

MOYAMOYA DISEASE - A RARE CASE REPORT OF YOUNG FEMALE

Dr. Ram Mohan Reddy T*, Sandeep Ankam, Prasamse M, Amer Quadri MD,
Dr. Ramya BalaPrabha

Abstract

Moyamoya disease is a rare cerebrovascular disease caused by progressive stenosis of distal internal carotid artery and their major branches. Moyamoya means puffy, hazy, obscure or vague, expressing the smoky look of vascular collateral network on angiography. The dilated and fragile basal collateral circulation display “PUFF OF SMOKE” appearance, thus called Moyamoya vessels. This case highlights the importance of considering Moyamoya disease as one of the differentials while dealing with patients with recurrent headaches. Use of CT angiography as an alternative diagnostic imaging tool for diagnosing Moyamoya in cases of MRI non-availability. Cerebral Angiography remains the gold standard for these patients but which was not considered here.

Keywords: Moyamoya disease, Puff of Smoke, Cerebral Angiography.